Primary tumors of the heart are rare, their morbidity is 0.0017-0.25% at autopsy. About seventy five percent of primary cardiac neoplasms are benign. Atrial myxomas are the most commonly encountered benign cardiac neoplasms. The other benign
tumors
are
fibroma, lipomatous tumor, valvular fibroelastic papilloma, and rhabdomyoma. Malignant neoplasms are about twenty-five percent of primary cardiac neoplasms, and the majority are angiosarcoma and rhabdomyosarcoma. Most cardiac osteosarcomas are
clinically mistaken for myxoma because of location in the left atrium. They are extremely rare, larger, tend to infiltrate, and very aggressive neoplasms. Histologically a variety of patterns may be encountered in addition to the osteosarcoma and
immunohistochemically cardiac osteosarcomas show similar features as noncardiac osteosarcomas. The overall prognosis of patients with these tumors is dismal. But the role of surgical palliation of these lesions remains valid. Therefore, we
believe
that
early diagnosis of cardiac sarcomas using echocardiography, as well as complete surgical excision, may improve survival.
Since we have experienced one case of primary osteosaroma of the left atrium, we report this with related references.
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